Cardiac myxoid neoplasm in a patient with suprarenal gland tumor: a Carney complex report




Anthonier C. Hinestroza-Newball, Departamento de Docencia e Investigación, Complejo Hospitalario Dr. Arnulfo Arias Madrid, Caja de Seguro Social, Panamá, Panamá
Zachary MacCammon-Broce, Facultad de Medicina, Universidad de Panamá, Panamá, Panamá
Kathiuska Bucktron, Facultad de Medicina, Universidad de Panamá, Panamá, Panamá
Belis A. Castillo-Hidalgo, Departamento de Docencia e Investigación, Complejo Hospitalario Dr. Arnulfo Arias Madrid, Caja de Seguro Social, Panamá, Panamá
Josué González-Mojica, Facultad de Medicina, Universidad de Panamá, Panamá, Panamá
Gerardo Victoria-Mirones, Servicio de Cirugía Cardiovascular, Departamento de Cirugía, Hospital Santo Tomás. Panamá, Panamá


Cardiac myxoid tumors are extremely rare with an annual incidence of 0.5 to 1 per million, with a female/male ratio of 3:1. Carney complex is an autosomal dominant endocrinopathy that includes Cushing’s syndrome, acromegaly, pigmented skin lesions, and myxomatous lesions in different organs. We report the case of a 33-year-old female patient with a history of adrenalectomy, for whom a chest computed tomography angiography incidentally showed the presence of a right intraventricular mass with involvement of the outflow tract. Surgical excision was decided upon, with subsequent biopsy with data suggestive of a cardiac myxoid neoplasm. Tumors associated with Carney complex are treated surgically on an individual basis.



Keywords: Myxoma. Carney complex. Neoplasms of the adrenal cortex. Adrenalectomy.